学术2015030马方综合征患者

(英文原文)TheRiskforTypeBAorticDissectioninMarfanSyndrome

BackgroundAorticdissectionsinvolvingthedescendingaortaareamajorclinicalprobleminpatientswithMarfansyndrome.

ObjectivesThepurposeofthisstudywastoidentifyclinicalparametersassociatedwithtypeBaorticdissectionandtodevelopariskmodeltopredicttypeBaorticdissectioninpatientswithMarfansyndrome.

MethodsPatientswiththediagnosisofMarfansyndromeandmagneticresonanceimagingor







































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